BASICS
DESCRIPTION
• Toxoplasmic chorioretinitis is usually a unifocal, full thickness chorioretinal lesion.
• Frequently arises from border of preexisting chorioretinal scar
• Associated with focal vitreous inflammation directly over the lesion
• Anterior segment findings may include mild iritis, large keratic precipitates, raised intraocular pressure.
• Signs and symptoms usually limited to the eye, cerebral form seen in HIV
EPIDEMIOLOGY
Incidence
• Majority of cases assumed to be congenital, although recent publications have challenged this
• There are documented reports of acquired disease in patients with a previously normal fundus and seronegative antibody titers.
Prevalence
• Most common cause of posterior uveitis
• Accounts for 90% of necrotizing retinitis
RISK FACTORS
• Ingestion of raw meat
• Exposure to cats
• HIV
GENERAL PREVENTION
• Avoid modifiable risk factors
• Consider using trimethoprim/sulfamethoxazole in patients with history of toxoplasmosis prior to cataract surgery
ETIOLOGY
• Infestation with an obligate intracellular protozoan, Toxoplasma gondii
• Parasite found in cats. Intermediate hosts include rodents and birds.
• Infestation is usually congenital (transplacental) and occasionally acquired.
• Predilection for the eye and brain.
COMMONLY ASSOCIATED CONDITIONS
• HIV
• Immunocompromised patients and the elderly
DIAGNOSIS
HISTORY
• Young healthy patients with recent onset of blurred vision.
– Photophobia
– Red eye
– Floaters
• Ingestion of raw meat that contains tissue cysts.
• Exposure to cats
• HIV or Immunocompromise
PHYSICAL EXAM
Common ophthalmic features of toxoplasmosis chorioretinitis can include:
• Decreased vision
• Floaters
• Conjunctival erythema
• Moderate to severe vitreous inflammatory reaction
• Focal area of chorioretinal inflammation
• Unilateral pale retinal lesion, with adjacent chorioretinal scar
• Mild anterior uveitis
• Raised intraocular pressure
• Optic disc swelling
Less common ophthalmic features include:
• Pain with severe iridocyclitis
• Large keratic precipitates
• Neuroretinitis with macular star formation
• Retinal artery or vein occlusion
• Cystoid macular edema
• Retinal vasculitis
• Peri-arterial exudation, Kyrieleis arteritis
DIAGNOSTIC TESTS & INTERPRETATION
Lab
Initial lab tests
• Serum IgM and IgG antibodies can be evaluated for presumed acquired infections
• IgM found 2 weeks to 6 months after initial infection
• High percentages of general population are IgG seropositive
• Can compare antibody levels in serum to intraocular fluid (aqueous or vitreous) to confirm intraocular production.
• Polymerase chain reaction (PCR) of the aqueous humor may be useful in atypical cases
• Chest x-ray, luetic screening, Toxocara serology, and TB testing may be helpful when the diagnosis is uncertain.
• HIV testing in atypical cases or patients at risk
DIFFERENTIAL DIAGNOSIS
• Syphilis
• Tuberculosis
• Toxocariasis
• Sarcoidosis
• Acute retinal necrosis (ARN)
• Endophthalmitis
– Endogenous
– Exogenous
TREATMENT
MEDICATION
First Line
Treatment plan based on location and severity
• Small non-sight threatening lesions
– Trimethoprim/sulfamethoxazole
– Second-generation tetracycline
• Sight threatening lesions near disc (2–3 mm) or in macula
– Pyrimethamine, PO 200 mg loading dose, then 25 mg PO daily
– Sulfadiazine 2 g PO loading dose, then 1 g PO q.i.d
– Folinic acid 10 mg PO every second day
Treatment duration is 5–6 weeks
• Steroids
– Low dose (20–60 mg PO daily 2–3 weeks)
– Required to reduce macular or optic nerve inflammation or swelling
– Start minimum of 24 hours after initiation of antibiotics
Discontinue 7–10 days prior to stopping antibiotics
Avoid periocular steroids as they may cause scleritis
• Topical medications: If anterior segment inflammation ± raised IOP
– Steroids, Prednisolone acetate 1% q.i.d
– Cycloplegic agent, Homatropine 2% t.i.d
– Antiglaucoma medications, Timolol maleate 0.5% b.i.d
Second Line
Sulfa allergy: Use Azithromycin, or Atovaquone, or Clindamycin.
ADDITIONAL TREATMENT
Additional Therapies
• Considerations for immunocompromised patients.
– Frequently subclinical inflammation
– May not have preexisting chorioretinal scars
– Multifocal ± bilateral disease can be seen
– Can be relentlessly progressive
– Cerebral form more common, patients require CNS imaging studies
– Delayed treatment can lead to diffuse spreading form mimicking ARN
– Avoid systemic steroid use
– May require long-term maintenance antibiotic therapy
Pregnancy Considerations
• Maternal fetal transmission can cause more severe ocular manifestations.
• Ophthalmic findings in the newborn
– Microphthalmos
– Bilateral macular scars
• CNS findings in the newborn
– Convulsions
– Paralysis
– Hydrocephalus
– Intracranial calcification
– Stillbirth
– Visceral involvement
• Pregnant women seronegative for Toxoplasmosis antibodies should avoid any contact with cats during pregnancy.
• Consult Obstetrician
• Treatment in Pregnancy:
– Clindamycin 300–600 mg PO q.i.d
– Spiramycin 3 g PO in 3–4 doses
– Do not use Pyrimethamine
SURGERY/OTHER PROCEDURES
Vitrectomy may be required for dense vitreitis or other complications such as retinal detachment.
ONGOING CARE
FOLLOW-UP RECOMMENDATIONS
• Small non-sight threatening lesions require less stringent follow-up care, but should be assessed 1 week after initiating therapy and then every 2 weeks.
• Sight threatening infections near the optic nerve or macula should be assessed at 3 days and then weekly.
• Usual course of treatment is 6 weeks.
• Avoid delays in treating immunocompromised patients and remember these patients may require long-term antibiotics.
Patient Monitoring
• All patients should have a complete dilated ocular exam on each visit.
• Results of all blood tests and ancillary testing should be attained as soon as possible.
• Patients on Pyrimethamine require weekly CBC testing.
• Fasting blood glucose levels should be determined prior to starting systemic steroid treatment.
DIET
• All patients should be instructed to avoid eating raw or undercooked meat containing Toxoplasma cysts.
• Other dietary risks include raw milk or unfiltered chlorinated surface water.
PATIENT EDUCATION
• All patients should be aware that the major routes of transmission are:
– Ingestion of contaminated foodstuffs; recommend adequate cooking of meat and care handling raw meat
– Contamination of hands from disposing of cat feces or contaminated soil or sand boxes; recommend gloves or hand washing
– Transplacental transmission from infected mother to fetus during gestation; pregnant women should avoid any contact with cats
PROGNOSIS
• 40% of patients may have permanent unilateral visual loss to 20/100 or less
• 90% of patients with macular lesions will experience severe vision loss
• 15% of patients may have mild visual loss (20/40–20/70)
• 5 year recurrence rate is ∼80%
• Vision loss more associated with duration of active episode than number of recurrences
COMPLICATIONS
• Mild to severe vision loss
• Vitreous hemorrhage
• Secondary choroidal neovascularization
• Epiretinal membrane formation
• Chronic and relentless vitreitis
• Retinal tear and detachment
• Cystoid macular edema
• Cataract
CODES
ICD9
• 130.2 Chorioretinitis due to toxoplasmosis
• 130.9 Toxoplasmosis, unspecified